Aetiology
RCM can be idiopathic or caused by mutations in genes related to sarcomeric proteins, but also infiltrative diseases, storage diseases, connective tissue disorders, hypereosinophilic syndrome and endomyocardial fibrosis.
- Genetic
- Primary RCM
- Drugs
- Hydroxychloroquine
- Ergotamine
- Methysergide
- Systemic disease
- Amyloidosis
- Sarcoidosis
- Friedrich’s ataxia
- Haemochromatosis
- Fabry’s disease
- Fibrosis
- Radiation
- Chemotherapy (e.g. anthracyclines)
- Malignancy
- Systemic sclerosis
- Diabetes mellitus
- Inflammatory/granulomatous
- Endomyocardial disease
- Endomyocardial fibrosis
- Carcinoid
- Hypereosinophillia
- Endocardial fibroelastosis
- Endocardial neoplasms
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