28th May 2025

A 25-year-old man is seen in neurological clinic.

A 25-year-old man is seen in neurological clinic. He has had a deterioration in his gait over the last ten years and requires a wheelchair due to poor balance. Over the last four months, his hearing has worsened. His family history is significant for his mother, aunt and maternal grandmother all having difficulty in walking as well as having hearing problems.

Select the SINGLE most likely diagnosis from the list below. Select ONE option only.