18th July 2023

You see a 23-year-old male in A&E complaining of acute onset tearing chest pain

You see a 23-year-old male in A&E complaining of acute onset tearing chest pain. He is above average height with long slender fingers. On examination of the mouth, he has a high-arched palate.

A defect in which of the following proteins is most likely to be implicated in this patient’s underlying condition?

Select the SINGLE most appropriate option from the list below. Select ONE option only.